Table 4 Comparison of auxiliary features between gPrD patients with FTD phenotype and FTD/prion disease

PSWCs on EEG, %

0/29 (0)

–

40/133 (30.1)

–

0.001

Positive CSF 14-3-3 protein, %

3/10 (30.0)

–

31/70 (44.3)

–

0.393

Elevated CSF tau protein, %

6/10 (60.0)

–

8/14 (57.1)

–

0.899

Positive RT-QuIC, %

2/3 (66.7)

–

–

–

–

Frontotemporal atrophy, %

26/29 (89.7)

51 (100.0)

4 (3.3)

0.044

< 0.001

Hyperintensity on MRI, %

6/24 (25.0)

0 (0)

113 (83.0)

< 0.001

< 0.001

Frontotemporal hypoperfusion or hypometabolism, %

10/11 (90.9)

35/36 (97.2)

19/32 (59.4)

0.417

0.054